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Page 1: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

329-0498 3311-1

0285-44-61920285-44-7217

2015 9

Page 2: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

-1-

1970 22 1-39

2013 2014 23

IG IGIG IG

23 100100 2013 2014 12 31

http://www.kawasaki-disease.net/kawasakidata/

1,9732014 10 10

14-50

1,973 30 1,9431,456 74.9

Excel 12132

1,456 950 65.253.1 95.7

2013 15,696 9,044 6,652 201415,979 9,097 6,882 31,675

7320-4 10 2013 302.5 340.1 262.9 2014 308.0 342.2 272.0

2014 0-4 10305.3 341.3 267.5

1.34 1.2822 2014 12

331,115 191,448 139,6671979 1982 1986

1990 200510,000 2006 1979 1.5

2010 12,000 1986

Page 3: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

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2013 15,000 1982

2013 0-4 10 302.5 2014308.0 2013 2014

15,5192013 1.54 2014 1.57

0-4

149-10

2013 20142009 2014

63.5 64.6 62.12013 2014 9-11

10 564.4 392.0 2011 20129-11 6-8

6-8 1.49

3,582 2,4042,256 2,183 0-4 102011-2012 2012 2013-14 2014

2014 2013 2013 20142013 2014

2011 2014100

0-4 10 20112012 2013

2014

78.5 78.4 78.7 1.9 2.11.8 19.5 19.5 19.5

200217

69.0 24.6 5.3 0.70.4

Page 4: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

-3-

592 1.9 338 1.9 254 1.9

315 193 122 1.01.1 0.9 146 163 6

1,329 4.2 796 4.4 533 3.9

0.030-5 6-11 1

1,339 4.2 871 4.8 468 3.52,696 8.5 1,785 9.8 911 6.7

822 2.6 575 3.2 247 1.8

15 1997-1998 232013-2014

3.27 0.620.39 0.07 0 0

6.30 1.161.05 0.19 0.01 0.01

1.48 0.81 0.27 0.20 0.03 0.01

2.7

IG25.0 64.3

68.460.9

Page 5: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

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IG 34.874.1 65.2

IGIG 92.6 92.6 92.5

IG 17.1

IG 11.7

16.784.5

5-9

IG 98.1

IG 1900-2099mg/kg 93.8 900-1099mg/kg 4.5 96.7 3.2

IG 1900-2099mg/kg 96.0 900-1099mg/kg 1.9 2100mg/kg+ 1.3 1700-1899mg/kg 0.6

2000mg/kg

IGIG 19.2 IG

IG 7.07

IG 1.01

IG 0.95

IG 0.51IG

IG 92.6

32.9

5.6

5.2

2.7

Page 6: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

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50 506-11 50

132 140136 2-4

10

4.4

31,675 2013 15,696 9,044 6,652 201415,979 9,097 6,882 1.34 2014 12331,115 191,448 139,667

0-4 10 2013 302.5 340.1 262.9 2014 308.0 342.2272.0 201414

9-102013 2014

2013 2014 9-11 10564.4 392.0 6-8

1.492013 2014

20132014

20112012 2013

2014

78.5 78.4 78.7 1.92.1 1.8 19.5 19.5 19.5

69.0 24.6 5.3 0.70.4

1.9 1.9 1.9315 193 122 1.0 1.1

0.9 146 163 64.2 4.4 3.9

0.030-5 6-11

4.2 3.270.62 0.39 0.07 0 0

8.5 6.301.16 1.05 0.19 0.01 0.01

Page 7: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

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2.6 1.48 0.81 0.27 0.20 0.03 0.01

25.0 64.3

IG 34.8

IG 92.6 92.6 92.5 IG 17.1

IG 11.7

16.7 84.55-9

IG 1900-2099mg/kg 93.896.7 2000mg/kg

IG 19.2 IG7.07 1.01 0.95

0.51 IG IG 92.632.9 5.6 5.2 2.7

g/dL50 50

6-11 50132 140

4.4

http://www.jichi.ac.jp/dph/kawasaki.html

1971.1975; 22 6 : 306-312.

1975; 5 12 : 22-29.1976; 34 2 : 275-283.

-1979; 20 7 : 755-757.

1981;22 1 : 53-58.

Page 8: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

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-1983; 24 1 : 53-58.

1985; 26 9 : 1049-1053.

1986; 37-51.1987; 28 9 : 1059-1066.

1988; 18-31.1990; 31 5 : 569-576.1992; 33 3 : 309-316.1994; 35 1 : 61-73.1996; 37 4 : 363-383.

1998; 61 3 : 406-420.2000; 63 1 : 121-132.2002; 65 2 : 332-342.

2002.2004; 67 2 : 313-323.2006; 69 2 : 281-292.

1989 20042007; 111 6 : 740-745.

2008; 71 2 : 349-360.20

2010; 73 1 : 143-156.21

2012; 75 3 : 507-523.22

2014; 77 2 : 271-290.Kawasaki T, Kosaki F, Okawa S, Shigematsu I, Yanagawa H. A new infantile acute febrilemucocutaneous lymph node syndrome MLNS prevailing in Japan. Pediatrics 1974; 54: 271-276.Yanagawa H, Kawasaki T, Shigematsu I. Nationwide survey on Kawasaki disease in Japan. Pediatrics1987; 80: 58-62.Yanagawa H, Nakamura Y, Yashiro M, Fujita Y, Nagai M, Kawasaki T, Aso S, Imada Y, ShigematsuI. A nationwide survey of Kawasaki disease in 1985-1986 in Japan. J Infect Dis 1988; 158 6 :1296-1301.Yanagawa H, Yashiro M, Nakamura Y, Kawasaki T, Kato H. Epidemiologic pictures of Kawasakidisease in Japan: From the nationwide survey in 1991 and 1992. Pediatrics 1995; 95 4 : 475-479.Yanagawa H, Yashiro M, Nakamura Y, Kawasaki T, Kato H. Results of 12 nationwideepidemiological incidence surveys of Kawasaki disease in Japan. Arch Pediatr Adolesc Med1995; 149: 779-783.Yanagawa H, Nakamura Y, Yashiro M, Ojima T, Koyanagi H, Kawasaki T. Update of theepidemiology of Kawasaki disease in Japan, From the results of 1993-94 nationwide survey. JEpidemiol 1996; 6 3 : 148-157.Yanagawa H, Nakamura Y, Yashiro M, Ojima T, Tanihara S, Oki I, Zhang T. Results of thenationwide epidemiologic survey of Kawasaki disease in 1995 and 1996 in Japan. Pediatrics 1998;102 6 : e65.Yanagawa H, Nakamura Y, Yashiro M, Oki I, Hirata S, Zhang T, Kawasaki T. Incidence survey ofKawasaki disease in 1997 and 1998 in Japan. Pediatrics 2001; 107 3 : e33.Nakamura Y, Yashiro M, Uehara R, Oki I, Watanabe M, Yanagawa H. Epidemiologic Featuresof Kawasaki Disease in Japan:Results from Nationwide Survey in 2005-2006. J Epidemiol2008; 18(4): 167-172.

Page 9: 1* B)¼ - 自治医科大学?>J>R>Y>E>N>R>[ Í / ë>L>_ Í ^ ] b$? Û @ j g _+« Ë @ Â } ? _ K S b [ G r [ _ } S4# d b1* B)¼ \ 3Q K ^ @ } Q b +0[ Ì M

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Nakamura Y, Yashiro M, Uehara R, Oki I, Watanabe M, Yanagawa H. Monthly observation of thenumbers of patients and incidence rates of Kawasaki disease in Japan: results from nationwidesurveys. J Epidemiol 2008; 18(6): 273-279.Nakamura Y, Yashiro M, Uehara R, Sadakane A, Chihara I, Aoyama Y, Kotani K, Yanagawa H.Epidemiologic features of Kawasaki disease in Japan: Results of the 2007-2008 nationwide survey.J Epidemiol 2010; 20(4): 302-307.Nakamura Y, Yashiro M, Uehara R, Sadakane A, Tsuboi S, Aoyama Y, Kotani K, Tsogzolbaatar EO,Yanagawa H. Epidemiologic features of Kawasaki disease in Japan: Results of the 2009-2010nationwide survey. J Epidemiol 2012; 22(2): 216-221.Makino N, Nakamura Y, Yashiro M, Ae R, Tsuboi S, Aoyama Y, Kojo K, Uehara R, Kotani K,Yanagawa H: Descriptive epidemiology of Kawasaki disease in Japan, 2011-2012: from the results ofthe 22nd nationwide survey. J epidemiol 2015; 25 3 :239-245.

32 35-39 Journal of Epidemiology http://www.jstage.jst.go.jp/article/jea/33 34 Pediatrics http://www.pediatrics.org/cgi/content/

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