194536359 referat osteosarcoma
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REFERAT
OSTEOSARCOMA
Presenter :
Rossi Monisa S.Ked
Pembimbing :
Dr. M.Tambah Thaibsyah Sp.B
Dr. Syafruddin Sp.B
Dr. Mufrizal Sp.B
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PENDAHULUAN
Osteosarkoma disebut juga osteogenik
sarkoma adalah suatu neoplasma ganas yang
berasal dari sel primitif (poorly differentiated
cells) di daerah metafise tulang panjang pada
anak-anak.
Radiografi diperlukan untuk mengetahui lokasi
dari lesi.
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Epidemiologi
Osteosarkoma 22% dari seluruhjenis tumor tulang.
Kanker tulang (osteosarkoma)sering
menyerang kelompok usia 1525tahun.
Etiologi masih belum jelas.
Lokasi osteosarkoma paling seringpada metafisis
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Tumor Frequency %
Telangiectatic 3.5-11
Parosteal 3-4
Periosteal 1-2
Gnathic 6-9
Small cell 1
Intraosseous, low grade
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Patofisiologi
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Gejala Klinis
Nyeri dan/ atau pembengkakan ekstremitasyang terkena.
Fraktur patologik.
Pembengkakan pada atau di atas tulang ataupersendian serta pergerakan yang terbata.
Teraba massa tulang dan peningkatan suhukulit di atas massa serta adanya pelebaran vena
Gejala-gejala penyakit metastatik meliputinyeri dada, batuk, demam, berat badanmenurun dan malaise.
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Predileksi Osteosarcoma
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Klasifikasi
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Klasifikasi
Osteosarkoma klasik.
Osteosarkoma hemoragi atau telangektasis
Parosteal osteosarkoma.
Periosteal osteosarkoma.
Osteosarkoma sekunder
Osteosarkoma intrameduler derajat rendah.
Osteosarkoma akibat radiasi.
Multifokal osteosarkoma.
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Stadium
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Laboratorium
RadiografiX-Ray, Ct-Scan, MRI,
Ultrasound, Nuclear Medicine
Patologi anatomi
Pemeriksaan Penunjang
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Perubahan periosteal berupa Codman triangles (white arrow) dan
masa jaringan lunak yang luas (black arrow).
X Ray
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Epitheloid Osteosarcoma
Telangiektasi Osteosarcoma
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Osteoblastoma like -
Condroblastoma like -
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Giant cell rich osteosarcoma
Osteosarcoma (fibrohistiocytic variant)
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Low-grade central osteosarcoma
Gnathic- Osteosarcoma
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Parosteal osteosarcoma
Multifocal osteosarcoma
Multifokal osteosarcoma
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Periosteal osteosarcoma
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Intracortical osteosarcoma.
High-grade surface osteosarcoma
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MRI
Gambaran MRI
menunjukkankortikal destruksi
dan adanya
massa jaringanlunak.
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Patologi Anatomi
Classic osteosarcoma in which there is abundant production of osteoid and bone
matrix in a lacy pattern into which the malignant cells are incorporated. Because
these sections usually are decalcified, the terms osteoid and immature bone are
interchangeable, especially if the imaging studies do not reveal the precise biopsy
site (H&E, 250).
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Diagnosa banding
1. Ewings sarcoma2. Osteomyelitis
3. Osteoblastoma
4. Giant cell tumor5. Aneurysmal bone cyst
6. Fibrous dysplasia
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Penatalaksanaan
Kemoterapi
Pembedahan
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