cas clinique patient 69 ans commercial retraitÉ tabac 15 pa; alcool+ fracture du coccyx adenome de...
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CAS CLINIQUE
PATIENT 69 ANS
•COMMERCIAL RETRAITÉ •TABAC 15 PA; ALCOOL+
•FRACTURE DU COCCYX •ADENOME DE LA PROSTATE
•TRAITEMENT = 0 •ALLERGIES = 0
MARS 2005:
THROMBOPHLEBITE PROFONDE DE LA JAMBE
INNOHEPPuis
PREVISCAN
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MAI 2005:
MULTIPLES POUSSEES PAPULO-NODULAIRES
INFILTREESNON DOULOUREUSES
DU VISAGE ET DU TRONC
PRECEDEES DEFIEVRE 38-39
ARTHRALGIESASTHENIE
DURANT 1 SEM
ARRET DU PREVISCAN
PERTE DE 7kg EN 6 SEM
Hb 10,3 g/dlLYMPHOCYTES 680/mm3
VS 85 mmCRP 40 mg/l
FERRITINE 800 μg/lIEPS: IgM MONOCLONAL λ
TDM TAP : NORMALFIBRO BRONCHES
FOGD, COLOSCOPIEMYELO, BOM
BIOPSIE CUTANEE: INFILTRAT LYMPHOCYTAIRE
TRAITEMENTS:PREDNISONE ½ mg/kg/j
COLCHICINEDAPSONE
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Quel est votre diagnostic ?
.
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BIOPSIE CUTANEE:INFILTRAT DERMO-HYPODERMIQUE
DIFFUSCELLULES MYELOIDES IMMATURES
BIOPSIE DE L’OREILLE:INFILTRAT
DERMO-HYPODERMO-PERICHONDRIQUE
MYELOGRAMME:PROBABLE MYELODYSPLASIE
TRAITEMENT:
PREDNISONE
THALIDOMIDE
AC ACETYLSAL
TRANSFUSIONS
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SYNDROME DE SWEET• + Sd MYELODYSPLASIQUE/ HEMOPATHIES: 20%
•SWEET ATYPIQUE •POLYCHONDRITE CHRONIQUE ATROPHIANTE •PRONOSTIC RESERVÉ; THALIDOMIDE?
DEVANT• SWEET CLINIQUE + INFILTRAT LYMPHO
PENSER A• UNE LOCALISATION CUTANEE D’UN Sd MYELODYSPLASIQUE
RECHERCHER• DES CELLULES MYELOIDES ATYPIQUES DANS
•LA PEAU•LE SANG PERIPHERIQUE
•LA MOELLE OSSEUSE
VIGNON-PENNAMEN MD et al. Arch Dermatol 2006;142:1170-1176.
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CAS CLINIQUE
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PATIENTE 25 ANS
•PROF DE LETTRES •VOYAGES EN EUROPE •TABAC-ALCOOL-DROGUE =0
•DERMATITE ATOPIQUE •UTERUS BICORNE •AGENESIE DU REIN DROIT
• GROSSESSE 7EME MOIS
IL Y A 18 MOIS
1 MOIS APRES ARRET DES C/O
LESION UNIQUE DE LA TEMPE
NFSCREATININE
URINESAUTO-ANTICORPS
BIOPSIE
DERMOCORTICOIDES
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LEISHMANIOSE CUTANEE
Reithinger R et al. Lancet Infect Dis 2007; 7:581–96.
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LEISHMANIOSE CUTANEE
• DIAGNOSTIC: COLORATION AU MGG
•TRAITEMENT: • GLUCANTIME • 20 mg/kg/j • EN 2 INJECTIONS IM/IV• 20-28 JOURS
REITHINGER R et al. Lancet Infect Dis 2007; 7:581–96.
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LEISHMANIOSE CUTANEEET GROSSESSE
•LESIONS VOLUMINEUSES ET EXOPHYTIQUES
•COMPLICATIONS FOETALES
•TRAITEMENT EN POST-PARTUM
MORGAN DJ et al. Clinical Infectious Diseases 2007; 45:478–82.