dr. humberto reyes b
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METABOLISMO DE LA BILIRRUBINA, PATOGENIA DE LAS ICTERICIAS. Dr. Humberto Reyes B. Síndrome de Criggler-Najjar : Déficit congénito de glucuronil transferasa Total (niño a la izquierda, con Kernicterus) Parcial (niño a la derecha). Laboratorio bioquímico hepático. - PowerPoint PPT PresentationTRANSCRIPT
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Dr. Humberto Reyes B.
METABOLISMO DE LA BILIRRUBINA,
PATOGENIA DE LAS ICTERICIAS
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Síndrome de Criggler-Najjar:
Déficit congénito de glucuronil transferasa
• Total (niño a la izquierda, con Kernicterus)•Parcial (niño a la derecha)
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Laboratorio bioquímico hepático
• Bilirrubinemia total y directa• Bilirrubina en orina• Aminotransferasas:
Transaminasa pirúvica (SGPT) (ALAT)Transaminasa oxaloacética (SGOT) (ASAT)
• Fosfatasas alcalinas• Gammaglutamil transpeptidasa (GGT)• Tiempo de protrombina• Albúmina sérica
Esquema hepatíticoEsquema colestásico
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