cardipatias congenitas
TRANSCRIPT
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CARDIOPATIAS CONGENITAS
Isabel Cristina CarmonaAngela Maria Cataño
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CARDIOPATIAS CONGENITAS
ANOMALIAS DEL CORAZÓN O DE LOS GRANDES VASOS PRESENTES DESDE EL NACIMIENTO. POR DEFECTOS DE LA EMBRIOGENESIS DURANTE LA 3 A 8 SEMANA DE GESTACIÓN.
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CLASIFICACIÒN
•INCOMPATIBLES CON LA VIDA INTRAUTERINA
•COMPATIBLES CON LA MADURACIÒN EMBRIOLOGICA Y EL NACIMIENTO.
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CARDIOPATIAS COMPATIBLES CON MADURACIÒN EMBRIOLOGICA Y NACIMIENTO
•DEFECTO DEL SEPTACIÒN•DTA O DTV•HIPOPLASIA VENTRICULO DERECHO O IZQUIERDO•FALTA DE CONEXIONES ESPECÌFICAS.
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FRECUENCIA DE MALFORMACIONES CARDIACAS
•Defecto tabique ventricular…………………….………. 42%•Defecto tabique auricular……………………............... 10%•Estenosis pulmonar ……………………………….…….. 8%•Conducto arterioso permeable………………………….. 7%•Tetralogia de fallot……………………………………..… 5%•Coartaciòn aortica………………………………………… 5%•Defectos tabique auriculoventricular………........... 4%•Estenosis aortica………………………………………….. 4%•Transposiciòn de los grandes vasos………….…….. 4%•Tronco arterioso………………………………………..…. 1%•Conexion venosa pulmonar anomala total……..… 1%•Atresia tricuspide…………………………………………1%
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FACTORES
•FACTORES GENÈTICOS : TRISOMIA 13, 18, 21, 15; SINDROME DE TURNER
•RUBEOLA CONGÈNITA
•TERATOGENOS
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ERRORES EN EL DESARROLLO EN LA MIGRACIÒN DEL TEJIDO
MESENQUIMATOSO
Anomalias del tracto de salida
Interrupciòn aislada del
cayado aortico Tronco
arterioso persistente
Tetralogia de fallot
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CATEGORIA DE LA ENFERMEDAD CARDIACA CONGÉNITA SEGÚN SU CLÍNICA.
•MALFORMACIONES QUE CAUSAN CORTO CIRCUITO IZQUIERDA- DERECHA
•MALFORMACIONES QUE CAUSAN CORTO CIRCUTO DERECHA- IZQUIERDA
•MALFORMACIONES QUE CAUSAN OBSTRUCCIÓN
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CORTOCIRCUITOS IZQUIERDA-DERECHA
DTA
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DTV
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CAP
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DEFECTO COMPLETO DEL CANAL AURICULOVENTRICULAR
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CORTOCIRCUITOS DERECHA-IZQUIERDA
TETRALOGIA DE FALLOT
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TRANSPOSICION DE LOS GRANDES VASOS
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TRONCO ARTERIOSO PERSISTENTE
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ATRESIA TRICUSPIDEA
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CVPAT (CONEXIÓN VENOSA PULMONAR ANOMALA TOTAL)
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ANOMALIAS CONGENITAS DE OBSTRUCCION
COARTACIÓN AORTICA
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ESTENOSIS Y ATRESIA PULMONAR
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ESTENOSIS Y ATRESIA AORTICAS